Treatment & Adherence

Treatment guidelines for cystic fibrosis

This is a non-exhaustive list

European Union

Best practice guidelines by the European Cystic Fibrosis Society (ECFS), 2018

This guideline is a revision of the ECFS best practice guidelines published in 2014, updating standards for best practice in key aspects of cystic fibrosis care.

Find out more


United Kingdom

Cystic fibrosis: diagnosis and management, 2017
The National Institute for Health and Care Excellence (NICE) guideline [NG78]

This guideline covers diagnosis and management of cystic fibrosis. It specifies how to monitor the condition and manage the symptoms to improve quality of life.

Find out more

This summary article of the guideline NG78 has been reviewed and approved by NICE, and is available in different languages:

Brazilian (Portuguese) | EnglishGermanSpanish | Polish


United States

Cystic fibrosis pulmonary guidelines, 2013 

Chronic medications for maintenance of lung health

Systematic review of guidelines by the Pulmonary Clinical Practice Guidelines Committee on chronic medications for the maintenance of lung health.

Find out more

Cystic fibrosis adult care, 2004 
Consensus conference report

Summary of the Cystic Fibrosis Foundation consensus conference in 1999 and information gathered since.

Find out more

Cystic Fibrosis Foundation pulmonary guidelines, 2018
Use of cystic fibrosis transmembrane conductance regulator modulator therapy in patients with cystic fibrosis

Cystic Fibrosis Foundation clinical practise guidelines endorsed by the American Thoracic Society.

Find out more



Brazilian guidelines for the diagnosis and treatment of cystic fibrosis, 2017

These guidelines from Grupo Brasileiro de Estudos de Fibrose Cística aggregate key scientific evidence to guide the management of patients across Brazil.

Find out more